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Road and parking lot construction in Madison, Wis. may result in travel delays and route changes to UW Health clinic and hospital locations. Please plan accordingly.Read more
Road and parking lot construction in Madison, Wis. may result in travel delays and route changes to UW Health clinic and hospital locations. Please plan accordingly.Read more
This is high blood pressure inside the blood vessels of the lungs. The walls of the blood vessels that supply the lungs may constrict or narrow, causing the pressure inside the blood vessels to increase. This can decrease the amount of blood that can move through the blood vessels of the lung to pick up oxygen that the body needs. The heart may need to work harder and harder to try and push more blood through the blood vessels to pick up oxygen with each breath. In time, the heart may not be able to keep up the increased work load, and you may become tired, dizzy, and short of breath. If the blood pressure in the blood vessels of the lung is not decreased, the heart may become damaged and perhaps even stop working.
Sometimes the cause is unknown, but there are some known causes:
Pulmonary arterial hypertension means high blood pressure in the arteries of the lungs. The right side of your heart pumps the blood into the arteries of your lungs. With this type, the right side of your heart has to work too hard to force blood through the lung vessels. The right side of the heart is not made to work so hard.
Pulmonary venous hypertension results in increased pressure in the veins of the lungs. A disease of the left side of the heart may cause increased pressure. Mitral valve disease or a damaged left ventricle may cause increased pressure in the veins, which leads to fluid build up in the lungs and high blood pressure.
Pulmonary hypertension from hypoxemia (low oxygen levels in the body) causes the blood vessels in the lung to become blocked. This affects the amount blood and oxygen flowing through your body. Emphysema, sleep apnea, or being exposed to high altitudes for a long time are a few causes.
Pulmonary hypertension due to chronic thrombotic and/or embolic disease is caused by blood clots or a blockage in the lungs. When blood clots in the lung form, blood flow is blocked and pressure builds up behind the blockage.
Other causes may be due to an illness where there is a direct affect on the blood vessels in your lung such as in pulmonary capillary disease or an inflammatory disease like sarcoidosis.
Because the symptoms are the same as those from many other diseases, it is often found by looking for and ruling out those other diseases.
Trouble breathing
Chest pain
Feeling dizzy
Fainting
Chronic fatigue
Swollen ankles and legs
Decreased ability to walk or exercise
Dry cough
Raynaud’s syndrome
If pressures inside the lungs increase, then symptoms get worse. Increased fatigue, increased ankle swelling, and fluid around
the lungs and the abdomen are present with
severe pulmonary hypertension.
This is a long-term disease. Although it cannot be cured, it can be managed. Discuss the treatment plans with your doctor:
Manage the cause. If you have a disease that caused the hypertension, that disease must be treated also.
Take medicines. Today, there are many medicines to help manage most people with pulmonary hypertension. You must know your medicines and how they should be taken.
Use oxygen. Low levels of oxygen in your blood will make the problem worse and increase the heart’s workload. Some patient’s need to wear oxygen in order to increase these levels.
Surgery can help correct congenital
heart problems (birth defects),
improve blood flow when old,
scarred blood clots are removed, and
repair or replace damaged heart
valves. Lung or heart/lung transplant
may be an option if other treatments
have failed.
Not every person with Pulmonary
Hypertension needs each of the medicines
listed below. Since each person is different,
their prescribed medicine plan may be
different.
Blood thinners
Types: Coumadin® (warfarin)
Function: This medicine makes the blood
less likely to clot or form a blockage.
Calcium channel blockers
Types: Nifedipine (Procardia®/Adalat®),
Amlodipine Besylate (Norvasc®), Diltiazem
Hydrochloride (Cardizem®, Cartia XT®)
Function: These work to decrease the
pressure inside the lungs of some people
with Pulmonary Arterial Hypertension.
Diuretics (“water pills”)
Types: Lasix (Furosemide®), Bumex
(Bumetanide®), Demadex (Torsemide®),
Aldactone (Spironolactone®) or metolazone
Function: These work to get rid of extra
body fluid.
Endothelin Receptor Antagonist
Types: Bosentan (Tracleer®), Ambrisentan
(Letairis®)
Function: This works to reduce the high
blood pressure in the blood vessels of the
lungs and may allow the heart to work
easier.
Phosphodiesterase Type 5- Inhibitors
Types: Sildenafil (Viagra® or Revatio®),
Tadalafil (Adcirca®)
Function: This works to reduce the high
blood pressure in the blood vessels of the
lungs and may allow the heart to work
easier.
Prostacyclin Analogue
Types: Epoprostenol (Flolan®, Veletri®)
Treprostinil (Remodulin®, Tyvaso®),
Ventavis (Iloprost®)
Function: These drugs directly dilate lung
blood vessels and reduce blood pressure in
the lungs. Flolan® is given by a nonstop
intravenous (IV) infusion. Remodulin® is
given through a constant subcutaneous
(under the skin) or IV infusion. Iloprost® is
inhaled (like a breathing treatment) every 2-
3 hours and Tyvaso® is inhaled 4 times
daily.
Low Sodium Diet
Because ingestion of salt (sodium chloride)
can increase water retention (“water weight
gain”), and water retention can increase
blood pressure, it is best if people with high
blood pressure limit their total daily intake
of salt (sodium chloride) to no more than
2,500mg. This may seem like a lot of salt
(sodium chloride) to be able to use from a
salt shaker and eat in a day, but salt is
contained both inside the salt shaker, as well
as hidden in foods we buy in the grocery
store. So, to limit the total daily intake of
salt (sodium chloride) to no more than
2,500mg, a person will need to add up the
total amount of salt (sodium chloride) from
all sources (salt shaker and within foods).
The amount of salt (sodium chloride) per
serving of food is often listed on the labels
of foods that are purchased in a grocery
store. Ask a doctor, dietician, pharmacist or
nurse for more information about this if you
have questions.
Supplemental Oxygen
If the doctor decides that adding
supplemental oxygen to your daily routine
would be helpful for you, using the way it is
prescribed may help to provide enough
oxygen for the best function of your body.
There is new research being done all the time and new treatments are being found.